August 24, 2010 — A novel sporadic prion protein disease, variably protease-sensitive prionopathy (VPSPr), with distinct features has been described as the first new prion disease since sporadic ...

Myoclonus is a sudden, random muscle jerk. It can happen alone or stem from a medical condition. Possible causes include medication side effects, damage to the nervous system, and disorders that ...

Prion infections lead to invariably fatal diseases of the CNS, including Creutzfeldt–Jakob disease (CJD) in humans, bovine spongiform encephalopathy (BSE), and scrapie in sheep. There have been ...

Sleep myoclonus is involuntary, nonrhythmic muscle twitching that occurs either as a person falls asleep or during sleep. The movements include hiccups, starts, and jerks. Sleep myoclonus is not a ...